Un rene… due uteri! La sindrome di Herlyn-Werner-Wunderlich
نویسندگان
چکیده
The case of an eleven-year-old girl with acute pelvic abdominal pain due to hematocolpos is presented. Herlyn-Werner-Wunderlich syndrome was finally diagnosed.
منابع مشابه
New Classification of Herlyn-Werner-Wunderlich Syndrome
BACKGROUND Uterus didelphys and blind hemivagina associated with ipsilateral renal agenesis are collectively known as Herlyn-Werner-Wunderlich syndrome (HWWS). In the literature, the syndrome often appears as a single case report or as a small series. In our study, we reviewed the characteristics of all HWWS patients at Peking Union Medical College Hospital (PUMCH) and suggested a new classific...
متن کاملScoliosis in Herlyn–Werner–Wunderlich Syndrome
Herlyn–Werner–Wunderlich syndrome (HWWS) is a congenital Müllerian duct anomaly characterized by uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. Little is reported about spinal deformity associated with this syndrome. This study presents a case of scoliosis occurring in the setting of HWWS and explores the possible association between the 2 diseases. A previously unrep...
متن کاملPyometra and Pregnancy with Herlyn-Werner- Wunderlich Syndrome Piometria e gravidez com síndrome de Herlyn-Werner- Wunderlich
Mullerian duct anomalies (MDAs) are congenital defects of the female genital system that arise from the abnormal embryological development of the Mullerian ducts.1,2 These abnormalities include a wide range of developmental anomalies, resulting from failure of development, defective fusion or defects in regression of the septum during fetal development. A review of the prevalence of different t...
متن کاملHerlyn-Werner-Wunderlich syndrome: a rare presentation with pyocolpos.
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA), also known as Herlyn-Werner-Wunderlich syndrome, is a rare syndrome with only a few hundred reported cases described since 1922. Only a handful of these cases have been associated with pyocolpos. Mullerian duct anomalies have an incidence of 2-3%. While OHVIRA constitutes 0.16-10% of these Mullerian duct anomalies. Symptoms usually p...
متن کاملHerlyn-Werner-Wunderlich syndrome: An unusual presentation with pyocolpos
Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly of the urogenital tract, which is characterized by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents at puberty with pelvic pain, dysmenorrhea, and a vaginal or pelvic mass. Although rare, it may present with purulent vaginal discharge due to secondary infection of the obstruct...
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ژورنال
عنوان ژورنال: Medico e bambino pagine elettroniche
سال: 2023
ISSN: ['2704-8268']
DOI: https://doi.org/10.53126/mebxxvif042